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Highlights & Basics
- Pulmonary stenosis is mostly congenital.
- Symptoms range from none to profound cyanosis and the potential for sudden death.
- Systolic ejection murmur is present and is loudest over left upper sternal border.
- Cyanotic patients are treated with oxygen and prostaglandin E1 prior to diagnostic testing.
- The diagnosis is confirmed and severity classified by echocardiography.
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Citations
Stout KK, Daniels CJ, Aboulhosn JA, et al. 2018 AHA/ACC guideline for the management of adults with congenital heart disease: a report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines. J Am Coll Cardiol. 2018 Aug 10 [Epub ahead of print].[Abstract][Full Text]
Otto CM, Nishimura RA, Bonow RO, et al. 2020 ACC/AHA Guideline for the management of patients with valvular heart disease: executive summary: a report of the American College of Cardiology/American Heart Association Joint Committee on Clinical Practice Guidelines. Circulation. 2021 Feb 2;143(5):e35-71.[Abstract][Full Text]
European Society of Cardiology. 2020 ESC guidelines for the management of adult congenital heart disease (previously grown-up congenital heart disease). Aug 2020 [internet publication].[Full Text]
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