Select a medication above to begin.
Thiola EC
tiopronin
Adult Dosing .
Dosage forms: DR TAB: 100 mg, 300 mg
cystinuria, severe homozygous
- [individualize dose PO tid]
- Start: 800 mg/day PO divided tid; Info: consider lower start dose in pts w/ severe toxicity hx w/ penicillamine; adjust dose to maintain urinary cystine levels <250 mg/L
renal dosing
- [see below]
- renal impairment: not defined, caution advised
- HD/PD: not defined, caution advised
hepatic dosing
- [not defined]
Peds Dosing .
- Dosage forms: DR TAB: 100 mg, 300 mg
cystinuria, severe homozygous
- [>20 kg]
- Dose: individualize dose PO tid; Start: 15 mg/kg/day PO divided tid; Max: 50 mg/kg/day; Info: consider lower start dose in pts w/ severe toxicity hx w/ penicillamine; adjust dose to maintain urinary cystine levels <250 mg/L
renal dosing
- [see below]
- renal impairment: not defined, caution advised
- HD/PD: not defined, caution advised
hepatic dosing
- [not defined]